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Pediatric Heart Center, Childrens Hospital, University of California at San Francisco, San Francisco, California
Accepted for publication July 2, 2007.
* Address correspondence to Dr Karl, Division of Pediatric Cardiac Surgery, University of California at San Francisco, 513 Parnassus Ave, San Francisco, CA 94143-0117 (Email: karlt{at}surgery.ucsf.edu).
Sickle cell disease in children requiring open heart surgical repair is uncommon and requires specific perioperative interventions to avoid complications from intravascular red cell sickling. We present a rare case of a 14-year-old girl with sickle cell disease and an anomalous right coronary artery from the pulmonary artery.
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