ATS
HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
QUICK SEARCH:   [advanced]


     

This Article
Right arrow Full Text
Right arrow Full Text (PDF)
Right arrow Alert me when this article is cited
Right arrow Alert me if a correction is posted
Right arrow Citation Map
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Add to Personal Folders
Right arrow Download to citation manager
Right arrow Author home page(s):
Nelson Alphonso
Andrew Newcomb
Christian P. Brizard
Andrew Cochrane
Right arrow Permission Requests
Citing Articles
Right arrow Citing Articles via HighWire
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by Alphonso, N.
Right arrow Articles by Cochrane, A.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by Alphonso, N.
Right arrow Articles by Cochrane, A.
Related Collections
Right arrow Congenital - cyanotic

Ann Thorac Surg 2005;80:1666-1671
© 2005 The Society of Thoracic Surgeons

Original article: Cardiovascular

Cor Triatriatum: Presentation, Diagnosis and Long-Term Surgical Results

Nelson Alphonso, MD * , Martin A. Nørgaard, MD, Andrew Newcomb, MD, Yves d'Udekem, MD, Christian P. Brizard, MD, Andrew Cochrane, MD

Victorian Pediatric Cardiac Surgery Unit, Royal Children's Hospital, Melbourne, Australia

Accepted for publication April 27, 2005.

* Address correspondence to Dr Alphonso, UCSF Department of Surgery, Division of Pediatric Cardiothoracic Surgery, 513 Parnassus Ave, Room S-549, Box 0117, San Francisco, CA 94143-0117 (Email: nelson.a{at}bigfoot.com).

BACKGROUND: Cor triatriatum sinister is a rare, surgically correctable, congenital cardiac anomaly. Fewer than 250 cases have been reported. It can occur as an isolated defect (classic) or in association with other congenital cardiac anomalies (atypical).

METHODS: A retrospective review of 28 consecutive patients diagnosed at the Royal Children's Hospital in Melbourne, Australia during a 22-year span from 1981 to 2003.

RESULTS: There were 13 men (46%) and 15 women (54%). Fifteen patients were less than 1 year of age (neonates, [n = 7], 25%; infants, [n = 8], 29%). 17 patients (61%) had a communication between the right atrium and either the proximal or distal chamber. Fifteen patients (54%) had atypical cor triatriatum. Median age at presentation was 6 months (range, 0.6 to 240). Twenty-four patients (86%) had presented by 5 years of age. Five patients (18%) underwent emergency surgery. Median age at operation was 7 months (range, 1 to 243). Twenty-seven patients (96%) underwent preoperative transthoracic echocardiography. Nine patients (32%), all with atypical cor triatriatum, required cardiac catheterization for diagnosis. Twenty-seven patients (96%) were correctly diagnosed before treatment. Twenty-seven patients (96%) were treated surgically. The defect was approached through the right atrium in 26 patients (93%). There was 1 early death and 1 patient died 10 years after repair. Follow-up was 86% complete. At a median follow-up of 98 months (range, 0.2 to 284), all patients including those with atypical cor triatriatum were in New York Heart Association's function class 1. Post-repair survival was 96% and 88% at 5 and 15 years, respectively.

CONCLUSIONS: Surgery offers good early and long-term results for both classic and atypical cor triatriatum.




This article has been cited by other articles:


Home page
 Ann. Thorac. Surg.Home page
C. Carr
Congenital Nomenclature: A Cause of Confusion During Literature Search
Ann. Thorac. Surg., August 1, 2007; 84(2): 716 - 716.
[Full Text] [PDF]


HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
ANN THORAC SURG ASIAN CARDIOVASC THORAC ANN EUR J CARDIOTHORAC SURG
J THORAC CARDIOVASC SURG ICVTS ALL CTSNet JOURNALS
Copyright © 2005 by The Society of Thoracic Surgeons.