ATS
HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
QUICK SEARCH:   [advanced]


     

This Article
Right arrow Full Text
Right arrow Full Text (PDF)
Right arrow Alert me when this article is cited
Right arrow Alert me if a correction is posted
Right arrow Citation Map
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Add to Personal Folders
Right arrow Download to citation manager
Right arrow Author home page(s):
Francis Robicsek
Right arrow Permission Requests
Citing Articles
Right arrow Citing Articles via HighWire
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by Fokin, A. A.
Right arrow Articles by Robicsek, F.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by Fokin, A. A.
Right arrow Articles by Robicsek, F.
Related Collections
Right arrow Chest wall

Ann Thorac Surg 2002;74:2218-2225
© 2002 The Society of Thoracic Surgeons

Review

Poland’s syndrome revisited

Alexander A. Fokin, MD, PhDa, Francis Robicsek, MD, PhDa*

a The Department of Thoracic and Cardiovascular Surgery, Carolinas Heart Institute, Carolinas Medical Center, Charlotte, North Carolina, USA

* Address reprint requests to Dr Robicsek, Dept. of Thoracic and Cardiovascular Surgery, Carolinas Medical Center, 1001 Blythe Blvd #300, Charlotte, NC 28203, USA
e-mail: tjohn{at}sanger-clinic.com

Poland’s syndrome is a rare congenital anomaly characterized by unilateral chest wall hypoplasia and ipsilateral hand abnormalities. Literary data suggest its sporadic nature. The prevailing theory of its cause is hypoplasia of the subclavian artery or its branches, which may lead to a range of developmental changes. The incidence of Poland’s syndrome varies between groups (male versus female patients, congenital versus familial cases, and so on) and ranges from 1 in 7,000 to 1 in 100,000 live births. Cases of Poland’s syndrome associated with leukemia, carcinoma of the hypoplastic breast, and other conditions, confirm the relationship between developmental defects and tumors, and require oncologic awareness. Various manifestations, age, and gender require different surgical approaches. Our experience, which includes 27 patients (15 male, 12 female), 20 of whom (12 male, 8 female) underwent operation, suggests that the repair should be done in two stages in children and in a single stage in adults. Reconstruction and/or stabilization of the aplastic ribs may be achieved using bone grafts or prosthetic mesh. Muscle flaps and breast implants may be used to correct muscle deficiency and breast hypoplasia and to help achieve a complete cosmetic repair.




This article has been cited by other articles:


Home page
 J. Thorac. Cardiovasc. Surg.Home page
A. Eroglu, D. Yildiz, and H. Tunc
Dextrocardia is a component of left-sided Poland syndrome
J. Thorac. Cardiovasc. Surg., November 1, 2005; 130(5): 1471 - 1472.
[Full Text] [PDF]

Home page
 Obstet GynecolHome page
D. Paladini, M. R. D'Armiento, and P. Martinelli
Prenatal Ultrasound Diagnosis of Poland Syndrome
Obstet. Gynecol., November 1, 2004; 104(5): 1156 - 1159.
[Abstract] [Full Text] [PDF]


HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
ANN THORAC SURG ASIAN CARDIOVASC THORAC ANN EUR J CARDIOTHORAC SURG
J THORAC CARDIOVASC SURG ICVTS ALL CTSNet JOURNALS
Copyright © 2002 by The Society of Thoracic Surgeons.