ATS
HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
QUICK SEARCH:   [advanced]


     

This Article
Right arrow Full Text
Right arrow Full Text (PDF)
Right arrow Alert me when this article is cited
Right arrow Alert me if a correction is posted
Right arrow Citation Map
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Add to Personal Folders
Right arrow Download to citation manager
Right arrow Permission Requests
Citing Articles
Right arrow Citing Articles via HighWire
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by Kirshbom, P. M.
Right arrow Articles by Spray, T. L.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by Kirshbom, P. M.
Right arrow Articles by Spray, T. L.
Related Collections
Right arrow Congenital - acyanotic

Ann Thorac Surg 2002;74:1616-1620
© 2002 The Society of Thoracic Surgeons

Original article: cardiovascular

Preoperative pulmonary venous obstruction affects long-term outcome for survivors of total anomalous pulmonary venous connection repair

Paul M. Kirshbom, MDa, Richard J. Myung, MDa, J. William Gaynor, MDa*, Richard F. Ittenbach, PhDb, Stephen M. Paridon, MDc, William M. DeCampli, MDa, Tom R. Karl, MDa, Thomas L. Spray, MDa

a Division of Pediatric Cardiac Surgery, The Cardiac Center at The Children’s Hospital of Philadelphia, Philadelphia, Pennsylvania, USA
b Division of Biostatistics and Epidemiology, The Cardiac Center at The Children’s Hospital of Philadelphia, Philadelphia, Pennsylvania, USA
c Division of Cardiology, The Cardiac Center at The Children’s Hospital of Philadelphia, Philadelphia, Pennsylvania, USA

* Address reprint requests to Dr Gaynor, Division of Cardiothoracic Surgery, The Children’s Hospital of Philadelphia, 34th St and Civic Center Blvd, Suite 8527, Philadelphia, PA, 19104, USA.
e-mail: gaynor{at}email.chop.edu

Presented at the Poster Session of the Thirty-eighth Annual Meeting of The Society of Thoracic Surgeons, Fort Lauderdale, FL, Jan 28–30, 2002.

BACKGROUND: Early outcomes after repair of total anomalous pulmonary venous connection continue to improve; however, little information is available concerning long-term functional status and quality of life.

METHODS: One hundred patients underwent isolated total anomalous pulmonary venous connection repair at The Children’s Hospital of Philadelphia between 1983 and 2001. Medical records were reviewed and a standardized questionnaire was administered to guardians of survivors.

RESULTS: Median age at repair was 15.5 days (range, 1 to 563 days). Overall hospital mortality was 14%, decreasing from 19% before 1995 to 5% after 1995. At 15 years after repair, actuarial survival was 84% and freedom from late death or reintervention for hospital survivors was 85%. At a median follow-up of 5.9 years (range, 0 to 17.7 years) 64% of guardians described their child’s overall health as excellent, 27% good, 9% fair, and 0% poor. With regard to school performance, 40% of children were characterized as above average, 29% average, 4% below average, and 27% were in special education classes or had repeated grades. By multivariable logistic regression, the presence of associated chromosomal or noncardiac syndromes and pulmonary venous obstruction were found to be significant factors with regard to parental assessment of both overall health and school performance.

CONCLUSIONS: The majority of children who undergo isolated total anomalous pulmonary venous connection repair can expect an excellent long-term functional outcome. Factors present before operation, such as pulmonary venous obstruction and associated anomalies, can influence overall health and school performance in the long term.




This article has been cited by other articles:


Home page
 RadiologyHome page
A. M. Gaca, J. J. Jaggers, L. T. Dudley, and G. S. Bisset III
Repair of Congenital Heart Disease: A Primer--Part 2
Radiology, July 1, 2008; 248(1): 44 - 60.
[Abstract] [Full Text] [PDF]

Home page
 PediatricsHome page
A. J. Shillingford, M. M. Glanzman, R. F. Ittenbach, R. R. Clancy, J. W. Gaynor, and G. Wernovsky
Inattention, Hyperactivity, and School Performance in a Population of School-Age Children With Complex Congenital Heart Disease
Pediatrics, April 1, 2008; 121(4): e759 - e767.
[Abstract] [Full Text] [PDF]

Home page
 PediatricsHome page
D. E. Creighton, C. M.T. Robertson, R. S. Sauve, D. M. Moddemann, G. Y. Alton, A. Nettel-Aguirre, D. B. Ross, I. M. Rebeyka, and and the Western Canadian Complex Pediatric Therapi
Neurocognitive, Functional, and Health Outcomes at 5 Years of Age for Children After Complex Cardiac Surgery at 6 Weeks of Age or Younger
Pediatrics, September 1, 2007; 120(3): e478 - e486.
[Abstract] [Full Text] [PDF]

Home page
 J. Thorac. Cardiovasc. Surg.Home page
M. G. McBride, P. M. Kirshbom, J. W. Gaynor, R. F. Ittenbach, G. Wernovsky, R. R. Clancy, T. B. Flynn, D. M. Hartman, T. L. Spray, R. E. Tanel, et al.
Late cardiopulmonary and musculoskeletal exercise performance after repair for total anomalous pulmonary venous connection during infancy
J. Thorac. Cardiovasc. Surg., June 1, 2007; 133(6): 1533 - 1539.
[Abstract] [Full Text] [PDF]

Home page
 J. Thorac. Cardiovasc. Surg.Home page
G. Y. Alton, C. M.T. Robertson, R. Sauve, A. Divekar, A. Nettel-Aguirre, S. Selzer, A. R. Joffe, I. M. Rebeyka, D. B. Ross, and Western Canadian Complex Pediatric Therapies Proje
Early childhood health, growth, and neurodevelopmental outcomes after complete repair of total anomalous pulmonary venous connection at 6 weeks or younger
J. Thorac. Cardiovasc. Surg., April 1, 2007; 133(4): 905 - 911.
[Abstract] [Full Text] [PDF]

Home page
 CirculationHome page
T. Karamlou, R. Gurofsky, E. Al Sukhni, J. G. Coles, W. G. Williams, C. A. Caldarone, G. S. Van Arsdell, and B. W. McCrindle
Factors Associated With Mortality and Reoperation in 377 Children With Total Anomalous Pulmonary Venous Connection
Circulation, March 27, 2007; 115(12): 1591 - 1598.
[Abstract] [Full Text] [PDF]

Home page
 Ann. Thorac. Surg.Home page
D. L.S. Morales, B. E. Braud, J. H. Booth, D. E. Graves, J. S. Heinle, E. D. McKenzie, and C. D. Fraser Jr
Heterotaxy Patients With Total Anomalous Pulmonary Venous Return: Improving Surgical Results
Ann. Thorac. Surg., November 1, 2006; 82(5): 1621 - 1628.
[Abstract] [Full Text] [PDF]

Home page
 Ann. Thorac. Surg.Home page
M. S. Cohen, A. H. Schultz, Z.-Y. Tian, D. D. Donaghue, P. M. Weinberg, J. W. Gaynor, and J. Rychik
Heterotaxy Syndrome with Functional Single Ventricle: Does Prenatal Diagnosis Improve Survival?
Ann. Thorac. Surg., November 1, 2006; 82(5): 1629 - 1636.
[Abstract] [Full Text] [PDF]

Home page
 J. Thorac. Cardiovasc. Surg.Home page
J. Meadows, A. C. Marshall, J. E. Lock, M. Scheurer, P. C. Laussen, and E. A. Bacha
A hybrid approach to stabilization and repair of obstructed total anomalous pulmonary venous connection in a critically ill newborn infant
J. Thorac. Cardiovasc. Surg., April 1, 2006; 131(4): e1 - e2.
[Full Text] [PDF]

Home page
 J. Thorac. Cardiovasc. Surg.Home page
P. M. Kirshbom, T. B. Flynn, R. R. Clancy, R. F. Ittenbach, D. M. Hartman, S. M. Paridon, G. Wernovsky, T. L. Spray, and J. W. Gaynor
Late neurodevelopmental outcome after repair of total anomalous pulmonary venous connection
J. Thorac. Cardiovasc. Surg., May 1, 2005; 129(5): 1091 - 1097.
[Abstract] [Full Text] [PDF]

Home page
 Ann. Thorac. Surg.Home page
C. L. Hancock Friesen, D. Zurakowski, R. R. Thiagarajan, J. M. Forbess, P. J. del Nido, J. E. Mayer, and R. A. Jonas
Total Anomalous Pulmonary Venous Connection: An Analysis of Current Management Strategies in a Single Institution
Ann. Thorac. Surg., February 1, 2005; 79(2): 596 - 606.
[Abstract] [Full Text] [PDF]

Home page
 ICVTSHome page
M. Ando, Y. Takahashi, and T. Kikuchi
Total anomalous pulmonary venous connection with dysmorphic pulmonary vein: a risk for postoperative pulmonary venous obstruction
Interactive CardioVascular and Thoracic Surgery, December 1, 2004; 3(4): 557 - 561.
[Abstract] [Full Text] [PDF]

Home page
 Arch Pediatr Adolesc MedHome page
P. Moons, K. Van Deyk, W. Budts, and S. De Geest
Caliber of Quality-of-Life Assessments in Congenital Heart Disease: A Plea for More Conceptual and Methodological Rigor
Arch Pediatr Adolesc Med, November 1, 2004; 158(11): 1062 - 1069.
[Abstract] [Full Text] [PDF]

Home page
 J. Thorac. Cardiovasc. Surg.Home page
K. Maeda, S. Yamaki, M. Yokota, A. Murakami, and S. Takamoto
Hypoplasia of the small pulmonary arteries in total anomalous pulmonary venous connection with obstructed pulmonary venous drainage
J. Thorac. Cardiovasc. Surg., February 1, 2004; 127(2): 448 - 456.
[Abstract] [Full Text] [PDF]


HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
ANN THORAC SURG ASIAN CARDIOVASC THORAC ANN EUR J CARDIOTHORAC SURG
J THORAC CARDIOVASC SURG ICVTS ALL CTSNet JOURNALS
Copyright © 2002 by The Society of Thoracic Surgeons.