HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS		QUICK SEARCH:   [advanced] Author: Keyword(s): Year:  Vol:  Page:

This Article Alert me when this article is cited Alert me if a correction is posted Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Personal Folders Download to citation manager Permission Requests Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Google Scholar Articles by Marmon, L. M. Articles by Dunn, J. M. Search for Related Content PubMed PubMed Citation Articles by Marmon, L. M. Articles by Dunn, J. M.

The Annals of Thoracic Surgery, Vol 38, 146-150, Copyright © 1984 by The Society of Thoracic Surgeons

ARTICLES

Congenital cardiac anomalies associated with the DiGeorge syndrome: a neonatal experience

LM Marmon, RK Balsara, R Chen and JM Dunn

The DiGeorge syndrome is a rare congenital abnormality of absent of hypoplastic thymus and parathyroid glands. Thirty neonates who had cardiac lesions and the DiGeorge syndrome are reviewed. The early mortality for 10 neonates undergoing palliative procedures was 80%. Seventy-five percent of the deaths were secondary to sepsis. Twenty neonates did not undergo palliative procedures. In this group, early mortality was 60% and late mortality was 65%. Sixty percent of the deaths in this group were associated with sepsis, with cardiac failure responsible for the remaining deaths. Survival in both groups has improved with appropriate treatment of the immunological and metabolic consequences of the DiGeorge syndrome.

This article has been cited by other articles:

				W. T. Mahle, J. Crisalli, K. Coleman, R. M. Campbell, V. K. H. Tam, R. N. Vincent, and K. R. Kanter Deletion of chromosome 22q11.2 and outcome in patients with pulmonary atresia and ventricular septal defect Ann. Thorac. Surg., August 1, 2003; 76(2): 567 - 571. [Abstract] [Full Text] [PDF]