The Annals of Thoracic Surgery, Vol 24, 498-507, Copyright © 1977 by The Society of Thoracic Surgeons
Surgical management of congenital pulmonary valve dysplasia
L Watkins Jr, JS Donahoo, D Harrington, JA Haller Jr and CA Neill
Pulmonary valvular stenosis secondary to congenital valve dysplasia differs
markedly from the classic variety of pulmonary stenosis. The reported
mortality of patients treated by standard commissurotomy is 38 to 66%. The
clinical features and operative management of 14 patients with dysplastic
pulmonary valves are reviewed. Three groups of patients were studied. Group
1 consisted of 5 patients treated by commissurotomy. Group 2 comprised 3
patients treated by partial excision of the valve. In neither group were
there operative deaths, but 5 of the 8 patients developed recurrent
stenosis; 3 required reoperation. In 1975, because of the high incidence of
recurrent stenosis, total valvectomy was begun. Ten patients (Group 3) have
undergone valvectomy with 1 death. Nine patients were doing well at 3 to 15
months of follow-up. Based on the reported mortality and present findings,
total excision of the valve is recommended for relief of stenosis in
pulmonary valve dysplasia.