The Annals of Thoracic Surgery, Vol 20, 461-467, Copyright © 1975 by The Society of Thoracic Surgeons
Surgical correction of unusual double-outlet right ventricle
WC Geldof, J Rohmer, A Oppenheimer-Dekker, Z Aytug and AG Brom
This paper presents the case history of an 8-year-old girl who had total
situs inversus and double-outlet right ventricle with pulmonary stenosis
and severe tricuspid insufficiency in the presence of dextrocardia with
ventricular discordance. A successful repair was performed using the
Rastelli technique in conjunction with replacement of the tricuspid valve
with a Bjork-Shiley prosthesis. The postoperative course was uneventful,
and follow-up catheterization revealed a good operative result. However,
the patient died suddenly during an emotionally upsetting period about two
months after the operation. Postmortem examination revealed only signs of
moderately severe cardiac decompensation. Some anatomical and embryological
comments are made.